Sturge–Weber Syndrome (SWS)

Figure 2.27 A: Sturge–Weber syndrome (Reprint from Burgdorf WH, Plewig G, Wolff HH, Landthaler M, eds. Braun-Falco’s Dermatology. 3rd ed. Heidelberg: Springer; 2009) B: Klippel–Trenaunay syndrome (Courtesy of Dr. Michelle B. Bain) C: Klippel–Trenaunay syndrome (Courtesy of Dr Michelle B. Bain)
Figure 2.27
A: Sturge–Weber syndrome
(Reprint from Burgdorf WH,
Plewig G, Wolff HH,
Landthaler M, eds. Braun-
Falco’s Dermatology. 3rd ed.
Heidelberg: Springer; 2009
)
B: Klippel–Trenaunay syndrome
(Courtesy of Dr. Michelle
B. Bain
)
C: Klippel–Trenaunay syndrome
(Courtesy of Dr Michelle
B. Bain
)
(Figure 2.27A)
  • Sporadic neurologic disorder, facial PWS associated with ipsilateral o cular and leptomeningeal anomalies
  • Facial PWS typically involves V1 distribution (can be more extensive or bilateral), congenital or acquired ocular abnormalities (glaucoma), neurologic abnormalities (seizures, motor dysfunction, mental retardation), intracranial “tram-track” calcification
  • 10–15% patients with PWS of V1 distribution have underlying SWS