Cutis Marmorata Telangiectatica Congenita

  • Onset at birth; typically improves with age
  • Presents with blanching reticulated vascular pattern on trunk/extremities with segmental distribution
  • Associated anomalies in ½ of patients (varicosities, nevus flammeus, macrocephaly, ulceration, hypoplasia, and/or hypertrophy of soft tissue and bone)